Congenital Ectodermal Dysplasia (Anhidrotic, Hypotrichotic, Anodontic Type). Presented by Capt. James H. Lockwood (MC), U.S.N., and (by invitation) Lt. L. K. Cowan (MC), U.S.N.
The patient, a white man aged 20, with "concave facies" presented sparse, thin hair over the scalp; hair was absent from the axillae, pubis, and body. The skin was smooth, thin, and dry. There was a milia-like eruption over the malar eminences. There was no evidence of sweating; the axillae were dry. Salivation appeared normal. The patient has anodontia. He has always been adversely affected by warm weather, being unable to sweat. The situation was made worse upon his entry into the United States Navy and his arrival for duty at Quantanamo Bay, Cuba. He developed anorexia, malaise, loss of weight, and recurrent dizzy spells accompanied by an erythematous flare of the skin over his face as a result of the chronic exposure to high temperatures of the tropical climate.
Beerman H, Luscombe HA. PHILADELPHIA DERMATOLOGICAL SOCIETY. AMA Arch Derm. 1960;81(3):486–489. doi:10.1001/archderm.1960.03730030144026
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