Diagnosis: Scleredema "Adultorum" (Buschke) in a Child. Presented by Dr. Frances Pascher and Dr. Lawrence Eanet (by invitation).
Three months ago a 9-year-old boy was noted by his parents to have rounding and fullness of the face. Six weeks later they became aware of tightness of the skin of the face, neck, arms, and torso. The patient himself voiced no complaints. There had been no recent febrile illness. Tonsillectomy was undergone 6 months previously. It is said that for the past 2 summers, persistent malar flush appeared after exposure to sunshine.On examination, the child appears healthy and well nourished. There is no fever. The facial skin shows nonpitting edema and induration to an extent that prevents full opening of the mouth. The skin of the neck, upper portion of the chest, upper portion of the back, the arms, and forearms feels hard and tight to the palpating fingers; the
Herrmann FJ, Silver H, Leider M. BRONX DERMATOLOGICAL SOCIETY. Arch Dermatol. 1961;84(5):853–857. doi:10.1001/archderm.1961.01580170147022
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