Only 3 reports of nevus lipomatosus cutaneus superficialis, a rare condition, have appeared in the American literature.1-3 In one of these the world literature was summarized.3
The disorder is a nevoid fatty growth adjacent to and perhaps arising from the walls of the blood vessels of the mid- and upper cutis. It usually is present at birth, appearing as yellow, somewhat linear, xanthoma-like papules, often on or near the pelvic girdle. The lesions may resemble an epidermal nevus in distribution.
Report of Cases
The patient was a 4-year-old white girl. At birth it was noted that she had tight, "scar-like" lesions almost in dermatomic distribution on the left abdominal wall. There were no symptoms. Growth of the lesions was proportionate to her development. It was observed that when she was straining at stool parts of the lesions would sometimes become red and remain so for about 24
ABEL R, DOUGHERTY JW. Nevus Lipomatosus Cutaneus Superficialis (Hoffman-Zurhelle): Report of Two Cases. Arch Dermatol. 1962;85(4):524–526. doi:10.1001/archderm.1962.01590040088013
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