[Skip to Content]
Access to paid content on this site is currently suspended due to excessive activity being detected from your IP address 34.237.138.69. Please contact the publisher to request reinstatement.
[Skip to Content Landing]
Article
November 1966

Keratoma Hereditaria Mutilans (Vohwinkel): Differentiating Features of Conditions With Constriction of Digits

Author Affiliations

NEW YORK

From the Department of Dermatology, New York University Schools of Medicine, New York.

Arch Dermatol. 1966;94(5):619-625. doi:10.1001/archderm.1966.01600290093015
Abstract

A patient with keratoma hereditaria multilans (KHM), a young white girl, presented the following classic features of this rare disease: familial palmar and plantar hyperkeratosis beginning early in life, starfish-like keratoses of the dorsa of hands and feet, linear keratoses of elbows and knees, and constriction of digits beginning in the teens. A classification of the hereditary and nonhereditary diseases which exhibit digital constriction is briefly presented. The majority of the hereditary diseases with digital constriction have palmar and plantar hyperkeratosis, whereas the nonhereditary conditions are usually not keratotic.

In addition to the usual KHM findings our patient presents a high-frequency hearing loss; an unusual, pseudopelade-type alopecia; and transient, plantar bullae.

The disease is probably a variant of mal de Meleda.

×