Aplasia cutis congenita is an uncommon entity and is very rarely found on the face. A girl had an unusual bilateral, symmetrically located aplasia cutis congenita of the temples, with a peculiar facies and a constellation of other cutaneous findings.
Aplasia cutis congenita is a rare dermatologic entity presenting in the newborn infant as localized areas of skin deficiency.1,2 Most often the affected area lies in the midline and posteriorly on the scalp and measures 1 to 2 cm in diameter. The defect is most often solitary, but multiple lesions may occur, which are usually symmetrically located. Aplasia cutis presents at birth as sharply marginated, raw, granulating wounds and may range in shape from circular to elongate, stellate, and triangular.3 These defects may reach enormous sizes, sometimes covering most of the scalp, and they are apt to be large when located on the trunk or limbs.4 The
Rudolph RI, Schwartz W, Leyden JJ. Bitemporal Aplasia Cutis Congenita: Occurrence With Other Cutaneous Abnormalities. Arch Dermatol. 1974;110(4):615–618. doi:10.1001/archderm.1974.01630100071018
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