A 27-year-old man had leukonychia totalis, multiple sebaceous cysts, and renal calculi. Pedigree analysis showed a total of four generations involved, with koilonychia additionally present in three of the affected individuals. Autosomal dominant inheritance is a postulation.
Bushkell LL, Gorlin RJ. Leukonychia Totalis, Multiple Sebaceous Cysts, and Renal CalculiA Syndrome. Arch Dermatol. 1975;111(7):899–901. doi:10.1001/archderm.1975.01630190089011
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