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August 1976

Natal Teeth and Steatocystoma Multiplex Complicated by Hidradenitis Suppurativa: A New Syndrome

Author Affiliations

From the Department of Dermatology, University of California, Irvine Medical School, Irvine.

Arch Dermatol. 1976;112(8):1132-1134. doi:10.1001/archderm.1976.01630320038010

• A new syndrome, consisting of natal or defective teeth, or both, steatocystomas of the skin, and epidermal cysts of the scalp, is described in several generations. One member of the family had eruptive molars. Male-to-male transmission suggests autosomal dominant inheritance. This syndrome should be separated from pachyonychia congenita I and II.

(Arch Dermatol 112:1132-1134, 1976)