THE LOS ANGELES DERMATOLOGICAL SOCIETY
March 12, 1975Marian M. Brubaker, MD, Recorder
Porphyria Cutanea Tarda With Sclerodermoid Changes. Presented by Perry Scholnick, MD, Norman Brooks, MD.
A 61-year-old man with a four-year history of tightening of the skin of the chest, neck, scalp, and arms has had occasional bullous lesions and fragility of the skin on the dorsa of the hands. There was no history of photosensitivity, except for mild burning of the eyes on exposure to sunlight. He had been a heavy consumer of alcohol for ten years, but not for the past three years. The important findings were hidebound skin on the anterior portion of the chest, neck, and scalp, with erosions on the dorsa of the hands. Conjunctival infection was present.Laboratory studies showed elevated levels of uroporphyrins (2,090 μg/24 hr; normal, <57 μg/24 hr) and coproporphyrins (348 μg/24 hr; normal, <234 μg/24 hr). The hematocrit reading was 42%, the serum iron value was 113 μg/100 ml (normal, 65
Brubaker MM. Society Transactions. Arch Dermatol. 1977;113(4):511–513. doi:10.1001/archderm.1977.01640040119021
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