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August 1978

Ichthyosiform Dermatosis and Deafness

Arch Dermatol. 1978;114(8):1243-1244. doi:10.1001/archderm.1978.01640200091039

To the Editor.—  I believe that there are more reported cases of the syndrome of ichthyosiform dermatosis and deafness as discussed by Baden and Alper (Archives 113:1701-1704, 1977). Very recently, Senter and colleagues1 added another case; they included in their summary a similar case of Salamon et al2 and three cases of Tay3 who clearly lack some of the predominant features. Still another patient who was described in 1975 by Pincus et al4 seems to belong to this group. In addition to the ichthyosiform skin disorder and neurosensory deafness, her patient demonstrates several of the other features common in this syndrome: loss of vision owing to progressive vascularization of the corneas; abnormalities of the hair, teeth, and nails; postnatal growth deficiency; and neuromuscular defects and recurrent skin infections.The patient in Pincus's case report is now 8 years old and has had hyperkeratotic and erythematous skin from

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