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December 1978

Cornoid Lamella in Pachyonychia Congenita

Author Affiliations

From the Division of Dermatology, University of Tennessee Center for the Health Sciences, Memphis. Dr Wilkin is now with the University of Texas Medical School, Houston.

Arch Dermatol. 1978;114(12):1795-1796. doi:10.1001/archderm.1978.01640240037012

• A 13-year-old white girl was admitted with pachyonychia congenita, Kumer and Loos type 1. In addition to all nails being distally elevated, plantar keratoses and bullae, and a scalloped tongue, the patient also had keratotic papules on the elbows and knees. A cornoid lamella was identified in the histologic examination of a keratotic papule.

The cornoid lamella, widely regarded as pathognomonic for porokeratosis (Mibelli) and its variants, may not be specific. This histologic marker should be sought in other localized disorders of keratinization.

(Arch Dermatol 114:1795-1796, 1978)