Tnilateral nevoid telangiectasia syndrome (UNTS) was first described by Zeisler in 1922 and a year later by Tommasi as single case reports.1,2 Since then, an additional 13 cases have been reported.3 The unilateral distribution of telangiectasias has been reported to be associated with pregnancy, puberty, alcoholism, cirrhosis, and as a congenital finding. We report a case of acquired UNTS in a prepubertal boy. This case raises questions about the role of estrogen in the pathogenesis of the syndrome.
Report of a Case
A healthy 15-year-old boy was seen in February 1978, in the Dermatology Clinic, Brooke Army Medical Center, Houston, for evaluation of a progressive eruption of three years' duration. There was no history of hepatitis or bronchitis. No family member has similar lesions. Examination showed a striking distribution of numerous vascular lesions that blanched on diascopy over the right upper anterior part of the chest, right shoulder,
Jucas JJ, Rietschel RL, Lewis CW. Unilateral Nevoid Telangiectasia. Arch Dermatol. 1979;115(3):359–360. doi:10.1001/archderm.1979.04010030061023
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