A patient has an acquired, scarring, bullous eruption. The severity of the cutaneous, ocular, esophageal, and laryngeal scarring was suggestive of cicatricial pemphigoid or the severely dystrophic forms of epidermolysis bullosa. Clinical features and histologic and immunofluorescence and electron microscopic study led to the diagnosis of epidermolysis bullosa acquisita. The spectrum of epidermolysis bullosa acquisita includes cases that closely approximate the severity of disease previously recognized only for the recessive form of epidermolysis bullosa dystrophica.
(Arch Dermatol 115:1325-1328, 1979)
Richter BJ, McNutt NS. The Spectrum of Epidermolysis Bullosa Acquisita. Arch Dermatol. 1979;115(11):1325–1328. doi:10.1001/archderm.1979.04010110031020
Customize your JAMA Network experience by selecting one or more topics from the list below.
Create a personal account or sign in to: