To the Editor.—
Goltz's syndrome or focal dermal hypoplasia is a well-established syndrome with multisystemic involvement characterized by cutaneous and skeletal deformities.1 The dermal hypoplasia is clinically manifested by several cutaneous features, including fawn-colored, soft nodules in areas of herniations of adipose tissue, skin depressions, and poikiloderma. Small papillomas are often noted on the distal extremities. The lack of literature concerning skin healing after injury with this syndrome prompted the reporting of this case.
Report of a Case.—
A 15-year-old girl who had Goltz's syndrome was surgically treated for a stress fracture of her left femur. Two large surgical incisions were required at sites of cutaneous lesions of focal dermal hypoplasia. Standard postsurgical care of the skin was administered with the addition of the liberal use of topical antibacterial creams. The cutaneous surface healed normally without complications, and healthy scar tissue developed on the incision site (Figure).Healed surgical
Burkhart CG. Goltz's Syndrome and Wound Healing. Arch Dermatol. 1983;119(3):187. doi:10.1001/archderm.1983.01650270005005
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