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September 1984

Epidermolysis Bullosa With Dysuria due to a Cicatricial Stricture of the Preputial Orifice

Author Affiliations

Department of Dermatology Hirosaki University School of Medicine 5 Zaifu-cho, Hirosaki 036, Japan

Arch Dermatol. 1984;120(9):1141. doi:10.1001/archderm.1984.01650450023010

To the Editor.—  In certain variants of epidermolysis bullosa dystrophica recessiva (EBDR), particularly in the Hallopeau-Siemens type and inversa type, repeated cutaneous and mucosal blistering, erosion formation and ulceration, as well as subsequent scarring may lead to various severe disorders.1 If the urinary tract is involved, various complications such as retention, subsequent bladder hypertrophy, hydroureter, hydronephrosis, and infection will develop. Although the development of severe urologic complications due to genital lesions in EBDR seems not so uncommon, only two patients with urinary tract involvement, to the best of our knowledge, have been described to date. Kretkowski2 has reported a case in a boy with dysuria secondary to meatal stenosis due to recurrent ulcerations on the glans penis. In this patient, a meatotomy was performed with successful improvement of dysuria. Shackelford et al3 have reported a case in a girl with external genital scarring, producing chronic vaginal reflex

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