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April 1985

Canestick Lesion of Vellus Hair in Netherton's Syndrome

Arch Dermatol. 1985;121(4):451. doi:10.1001/archderm.1985.01660040025006

To the Editor.—  Netherton's syndrome (ichthyosis linearis circumflexa) is a rare congenital ectodermal defect.1 At birth or shortly thereafter, the skin becomes erythematous and scaly. Later, serpiginous scaling appears on the trunk and proximal parts of the extremities. Associated features are lichinified dermatitis of the major skin flexures and short brittle scalp hair. Microscopic examination of the hair or a scalp biopsy specimen show the diagnostic defect tricorrhexis invaginata, also known as "bamboo hair defect" (Fig 1). In the present case the diagnosis was not made until the hair defect was observed in the thin vellus hair of the scalp. The finding, to our knowledge, has escaped photographic illustration in the literature, so that initially we thought it was an artifact or some fiber structure of nonhuman origin.

Report of a Case.—  A 7-year-old boy had skin and hair lesions but was otherwise normally developed. Shortly after birth he

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