To the Editor.—
Dermatologists are frequently confronted with cutaneous congenital disorders, but rarely are they confronted with malformations outside of their own speciality. The unusual case we report is of interest since it involves a nondermatologic malformation with a very misleading cutaneous symptomatology.
Report of a Case.—
A 13-year-old girl presented with erythema nodosum that had been ongoing for two weeks, buccal aphthous ulcerations, several skin ulcerations around the anus, polypoid formations suggestive of genital warts on the margin of the anus, and intermittent fever. In the vulvar area, the left labium major was swollen as in bartholinitis, and the hymen was intact. No drug therapy had been administered for four months.During childhood, the patient had suffered from recurrent urinary and vaginal infections. At 8 years of age, a mesangial IgA nephropathy was discovered. On admission, three diagnoses were considered: Crohn's disease, Behçet's disease, and child abuse, on the
Grob JJ, Collet AM, Bonerandi JJ. Dermatologic Manifestations Associated With an Anorectal Malformation. Arch Dermatol. 1987;123(10):1278–1279. doi:10.1001/archderm.1987.01660340038015
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