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April 1990

Congenital Erosive Dermatosis With Reticulated Supple Scarring: First Neonatal Report

Author Affiliations

Departments of Dermatology and Pediatrics University of Brest 29285 Brest Cedex, France

Arch Dermatol. 1990;126(4):544-546. doi:10.1001/archderm.1990.01670280130035

To the Editor.—  Congenital erosive dermatosis healing with reticulated supple scarring is a cutaneous and visceral syndrome concerning children who presented at birth with erosive and bullous lesions that healed afterward with reticulated scarring. Five cases have already been reported1,2., we report the first observation with a clinical aspect present at birth.

Report of a Case.—  A male newborn, the first child of parents without a history of consanguinity, was born after a 30-week gestation by cesarean delivery (birth weight, 1000 g; Apgar scores, 3 at 1 minute, 6 at 5 minutes; normal placenta). He presented at birth with a widespread erythematous dermatosis looking like "scalded skin." An adhesive membrane was noticed in places on the fetal skin, possibly corresponding to the early stage of amniotic sac adhesion; removal of this adhesion left erosive lesions in places, particularly on the face (Fig 1). The amniotic rupture occurred 5 days

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