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April 1993

Ectodermal Dysplasia in Cape Verdian Families

Author Affiliations

Department of Dermatology Boston University School of Medicine 80 E Concord St Boston, MA 02118

Arch Dermatol. 1993;129(4):515-516. doi:10.1001/archderm.1993.01680250131029

To the Editor.—  The term ectodermal dysplasia (ED) describes a group of inherited, nonprogressive disorders affecting skin and structures derived from embryonic ectoderm1 (primarily hair, teeth, nails, and sweat glands).Cape Verde is a cluster of islands in the Atlantic Ocean. Two immigrant families from Cape Verde are described with a newly defined form of ED.

Report of Cases.—Case 1.—  A 10-year-old girl had white spots on her skin for several years. She was otherwise healthy and active. One brother (out of nine siblings) reportedly had similar lesions.The examination revealed a child of normal size and intelligence for her age. Skin turgor and texture were normal, but there were multiple 2- to 5-mm depigmented macules on her extremities (Fig 1). The frontal hairline was considerably displaced toward the posterior aspect; the density was otherwise normal, and no shaft anomalies were appreciated on a hair mount examination.