Although phlebosclerosis of the portal system is recognized as a primary entity, its definition is obscure and its pathogenesis and etiology require further investigation. Since its occurrence has been adequately established,1 it should be more carefully sought for at autopsy. It is the purpose of this paper to indicate how it may be clinically identified more frequently. It is also proposed to employ henceforth the name "primary portal phlebosclerosis" for clarification and uniformity.
Up to 1928,2 29 cases were reported in children, but few in adults. The exact number is difficult to ascertain in view of the existing confusion. In many of these cases the condition appeared to resemble Banti's syndrome, as it did in my case. However, on further study or at autopsy, the question of some primary obstruction of the portal circulation, with or without coexisting thrombosis or sclerosis of either the splenic or the portal
REICH NE. PRIMARY PORTAL PHLEBOSCLEROSIS. Arch Intern Med (Chic). 1942;69(1):117–127. doi:10.1001/archinte.1942.00200130127012
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