In recent years a number of reports concerning congenital, complete heart block have appeared. Although this electrophysiological abnormality is often associated with congenital malformations of the heart, it may occur as an isolated entity. When heart block is not an isolated entity, the prognosis is determined primarily by the severity of associated anatomic abnormalities, or the presence or absence of Stokes-Adams attacks, or congestive heart failure.1 If the QRS duration is normal and if the ventricular rate is not excessively slow, the outlook for children with isolated congenital heart block appears to be good.2
Much less information is available in the literature concerning the natural history of congenital partial heart block, perhaps because a congenital basis often is difficult to prove. The patient described in this report has congenital, first degree heart block with an unusually long PR interval. Her problem represents an interesting therapeutic challenge and a
Waggoner DM, Wallace AG. Congenital Partial Heart Block. Arch Intern Med. 1968;122(1):66–68. doi:10.1001/archinte.1968.00300060068014
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