• A case of autoimmune pancytopenia is described in a patient with mannosidosis who developed anti-platelet and anti-neutrophil antibodies and a low haptoglobin level. Bone marrow biopsy and111InCl3 bone marrow scanning demonstrated hypoplasia of the marrow with a paucity of "storage cells." Pathogenic mechanisms and implications for other inborn errors of metabolism are discussed.
(Arch Intern Med 1983;143:1266-1268)
Press OW, Fingert H, Lott IT, Dickersin CR. Pancytopenia in Mannosidosis. Arch Intern Med. 1983;143(6):1266–1268. doi:10.1001/archinte.1983.00350060198036
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