• In the clinical course of a patient with progressive facial hemiatrophy associated with ipsilateral body atrophy (total hemiatrophy), signs and symptoms of localized scleroderma were noted. The patient subsequently was found to have Schönlein-Henoch purpura with renal involvement and, later, paroxysmal nocturnal hemoglobinuria. To our knowledge, such an association has not been reported before.
(Arch Intern Med 1985;145:731-733)
Kuto F, Sakaguchi T, Horasawa Y, Hayashi M, Hirasawa Y, Tokuhiro H. Total Hemiatrophy: Association With Localized Scleroderma, Schönlein-Henoch Nephritis, and Paroxysmal Nocturnal Hemoglobinuria. Arch Intern Med. 1985;145(4):731–733. doi:https://doi.org/10.1001/archinte.1985.00360040165035
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