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April 1985

Total Hemiatrophy: Association With Localized Scleroderma, Schönlein-Henoch Nephritis, and Paroxysmal Nocturnal Hemoglobinuria

Author Affiliations

From the Departments of Internal Medicine (Drs Kuto, Sakaguchi, Horasawa, and Tokuhiro) and Clinical Pathology (Drs Hayashi and Hirasawa), Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan.

Arch Intern Med. 1985;145(4):731-733. doi:10.1001/archinte.1985.00360040165035

• In the clinical course of a patient with progressive facial hemiatrophy associated with ipsilateral body atrophy (total hemiatrophy), signs and symptoms of localized scleroderma were noted. The patient subsequently was found to have Schönlein-Henoch purpura with renal involvement and, later, paroxysmal nocturnal hemoglobinuria. To our knowledge, such an association has not been reported before.

(Arch Intern Med 1985;145:731-733)