Historically, diseases of the central nervous system (CNS) have been named after individuals who first described them (eg, Dandy-Walker syndrome, named after Walter Dandy, MD, and Arthur Earl Walker, MD) or initially characterized by histological or clinical features (eg, DeMorsier septo-optic dysplasia, Alzheimer presenile dementia, or Pick frontotemporal dementia [FTD]). If affected patients had variable clinical presentations, the disorder might have been named descriptively, based on timing/onset of symptoms (such as relapsing-remitting multiple sclerosis) or affected parts of the CNS (such as neuromyelitis optica).
Desikan RS, Barkovich AJ. Hazards of Neurological Nomenclature: Observations From Neurodevelopmental and Neurodegenerative Disorders. JAMA Neurol. 2017;74(10):1165–1166. doi:10.1001/jamaneurol.2017.1747
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