Clinical history and pathologic findings are described in a disease occurring in two siblings and characterized by onset in childhood, subacute progression, movement disorder, increased muscle tone, and dysphagia. Pathologically, there is marked loss of neurons from the caudate nucleus and putamen. The disease is familial.
Roessmann U, Schwartz JF. Familial Striatal Degeneration. Arch Neurol. 1973;29(5):314–317. doi:10.1001/archneur.1973.00490290054005
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