In 1926, Roussy and Lévy described a hitherto undescribed entity which they called "dystasie aréflexique héréditaire." Thus far, no patient has come to postmortem examination, and the nosology of this disease has been a matter of controversy. The finding of numerous onion bulbs in the nerve biopsy specimen from one of Roussy and Lévy's original patients demonstrates that this entity is a form of hypertrophic neuritis.
Lapresle J, Salisachs P. Onion Bulbs in a Nerve Biopsy Original Case of. Arch Neurol. 1973;29(5):346–348. doi:10.1001/archneur.1973.00490290086013
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