To the Editor.—
The article on cerebral vasculitis by Snyder and McClelland (Arch Neurol 35:612-614, 1978) is interesting. No specific diagnosis was made and the condition was thought to be a "distinct entity." However, another diagnosis that was not included in the differential list and a condition that occurs in females is fibromuscular dysplasia.Several patients with fibromuscular dysplasia of the cervicocephalic system have demonstrated intracranial changes attributed to the same disease process. A patient with moyamoya disease and the typical angiographic appearance of fibromuscular dysplasia caused the authors to believe these two diseases were related.1 Cases that involve the intracranial portions of the carotid artery, with irregular constrictions and occlusions of the distal vessels and with no systemic arteriographic evidence of fibromuscular dysplasia (normal renal arteriogram as in the case reported), have shown the typical "string of beads" appearance.2.3 Cases with noticeable involvement of the renal and
Massey EW, Reader A. Cerebral Vasculitis. Arch Neurol. 1979;36(5):321. doi:10.1001/archneur.1979.00500410099020
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