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April 1980

'Ophthalmoplegia Plus' or Kearns-Sayre Syndrome?-Reply

Author Affiliations

Department of Pathology Medical Department Activity Ft Campbell, KY 42223
The G. N. Wilcox Memorial Hospital and Health Center, Inc 3420 Kuhio Hwy Lihue, HI 96766
The John A. Burns School of Medicine University of Hawaii 2444 Dole St Honolulu, HI 96822

Arch Neurol. 1980;37(4):256. doi:10.1001/archneur.1980.00500530094032

In Reply.—  Boltshauser and Rowland have identified certain similarities between the clinical course and neuropathologic features in our patient (Archives 36:481-484, 1979) and those described in instances of the Kearns-Sayre syndrome. Recent information in two references1.2 cited by Boltshauser, not captured in our original literature search, is particularly suggestive that reported instances of the juvenile form of spongy degeneration of the CNS, including ours, may in fact represent cases of the Kearns-Sayre syndrome.We regret that data concerning clinical and laboratory parameters mentioned by Boltshauser and Rowland are not available to us at this time and are not retrievable.