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June 1981

Linear Nevus Sebaceus Syndrome: Report of a Case With Lennox-Gastaut Syndrome Following Infantile Spasms

Author Affiliations

From the Departments of Pediatrics (Drs Kurokawa, Sasaki, Hanai, and Goya) and Radiology (Dr Komaki), Kyushu University, Fukuoka, Japan.

Arch Neurol. 1981;38(6):375-377. doi:10.1001/archneur.1981.00510060077015

• We report what we believe to be the first known case of linear nevus sebaceus syndrome with infantile spasms followed by Lennox-Gastaut syndrome. The EEG revealed hemihypsarrhythmia and then asymmetrical slow spike-wave complexes. A pneumoencephalogram showed dilation and distortion of the lateral ventricle ipsilateral to the facial nevus on the left side. A computerized tomographic scan disclosed low density in the left parietotemporal region, a feature not reported previously. The findings indicated extensive lateralized cerebral lesions.

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