Spinal segmental myoclonus (SSM) is characterized by involuntary, semirhythmic contractions of skeletal muscle groups innervated by a limited spinal cord region.1-10 It is usually not affected by sensory stimuli but rather is increased by fatigue and emotional stress and usually ceases with sleep.3,8,11 Patients with SSM do not have a generalized neurological disorder, and there are no associated EEG changes.1,2,8,11 The primary abnormality is in the spinal cord,3-8,11-13 and multiple etiologic factors have been implicated: infection,3,6,9,11,12 intramedullary and extramedullary tumors,1,4,7-9,14 trauma,4 osteoarthritic lesions,11 arteriovenous malformation,10 meningomyelocele,15 and degenerative motor system disease.11,13 Previously reported treatment has largely consisted of pharmacotherapy.8,11 We describe a patient with SSM due to cervical spondylosis cured by surgical decompression of the spinal cord. To our knowledge, this communication is the first to report successful surgical therapy for SSM.
REPORT OF A CASE
Daniel DG, Webster DL. Spinal Segmental Myoclonus: Successful Treatment With Cervical Spinal Decompression. Arch Neurol. 1984;41(8):898–899. doi:10.1001/archneur.1984.04050190108026
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