To the Editor.
—In an issue of the Archives, Gourie-Devi et al1 reported a benign form of anterior horn cell disease involving only, or mainly, one extremity and called this condition monomelic amyotrophy; similar cases have been reported by others,2-4 including a large series by Hirayama et al,5 who called their cases, which were limited to one upper extremity, juvenile spinal muscular atrophy of unilateral upper extremity.In 1978 we studied six similar cases and called the syndrome benign focal amyotrophy,6 which we believe describes better its course and localized presentation. In an issue of the Archives, Riggs et al7 reported one case in which the symptoms were limited to one lower extremity and used the same descriptive denomination. We believe that this term emphasizes the benign nature of the condition and does not exclude the fact that it could manifest itself in any extremity
Bertorini TE, Adornato BT, Kucera J. Benign Focal Amyotrophy. Arch Neurol. 1986;43(5):432. doi:https://doi.org/10.1001/archneur.1986.00520050012011
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