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Comment & Response
June 2014

Macular Caldera in North Carolina Macular Dystrophy: Only an Illusion of Posterior Pole Staphyloma

Author Affiliations
  • 1Department of Ophthalmology, Wilmer Eye Institute, Johns Hopkins University, Baltimore, Maryland
  • 2Northern California Retina Vitreous Associates, Mountain View

Copyright 2014 American Medical Association. All Rights Reserved. Applicable FARS/DFARS Restrictions Apply to Government Use.

JAMA Ophthalmol. 2014;132(6):786-787. doi:10.1001/jamaophthalmol.2014.1705

To the Editor We read with interest the article by Schoenberger and Agarwal titled “Intrachoroidal Cavitation in North Carolina Macular Dystrophy.”1 They describe 2 patients who had bilateral macular “staphylomas.” We disagree with the nomenclature (staphyloma) used to describe these advanced macular lesions and favor the term macular caldera, as previously explained by Khurana et al.2Staphyloma refers to a definite outpouching of the sclera that is lined with uveal tissue. Although Schoenberger and Agarwal demonstrate with optical coherence tomography (OCT) the posterior bowing of the central macula, the entire sclerochoroidal interface is not well visualized on their conventional spectral-domain OCT.