A man in his 30s presented with history of exudative retinopathy in the setting of retinitis pigmentosa. This entity is typified by retinal telangiectasias, lipid exudation, and potential neovascularization, but differs from classic Coats disease in its predilection for bilateral involvement, age at presentation, familial association, and predominantly inferior distribution (Figure).1,2 This patient had a history of vitreous hemorrhage and significant cataract and underwent pars plana vitrectomy and lensectomy in the right eye. Subsequently, he had progression of his exudative response in his postoperative course. The refractile objects in the photographs are cholesterol crystals throughout the unicameral eye.
Jiang Y, Lim J, Janowicz M. Cholesterol Crystals Secondary to Coats-Like Response With Retinitis Pigmentosa. JAMA Ophthalmol. 2017;135(10):e173132. doi:10.1001/jamaophthalmol.2017.3132
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