The patient is a 42-year-old man who was noted to have tangles of dilated, intertwined, and tortuous retinal vessels of his right eye on fundus examination. On examination, Snellen visual acuity was 20/20 OU, and intraocular pressure was within normal limits. Fluorescein angiography (Figure) demonstrated retinal arteriovenous malformation with no evidence of leakage of dye from the vessels. A diagnosis of racemose angioma was made. Magnetic resonance imaging of the brain and orbits did not demonstrate any underlying arteriovenous malformations. Multiple follow-up evaluations have revealed a stable course, and the patient continues to remain otherwise asymptomatic. Congenital retinal arteriovenous malformations (racemose angioma) are associated with ipsilateral intracranial or interosseous vascular malformations that can spontaneously hemorrhage, in a condition called Wyburn-Mason syndrome.1 In the eye, the findings are usually stable and benign.2
Reed DS, Mehta A, Drayna P. Isolated Racemose Angioma—A Rare Retinal Condition. JAMA Ophthalmol. Published online August 01, 2019137(8):e185512. doi:10.1001/jamaophthalmol.2018.5512
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