A 2-year-old girl presented with exotropia. Clinical examination results disclosed a diffuse retinal cavernous hemangioma (Figure) that was treated with laser photocoagulation when progressive leakage was detected. No other lesions were found on liver and brain magnetic resonance imaging. In a case report of a pediatric retinal cavernous hemangioma, similar findings were identified in a 4-year-old girl.1 Familial cases have been described in the literature2,3 and have been associated with KRIT-1 and CCM1 sequence variants.4