A 6-year-old girl with mucopolysaccharidoses type 1 with a Hurler-Scheie phenotype, who was receiving weekly enzyme replacement therapy, presented for an ophthalmological evaluation. Her best-corrected visual acuity was 20/50 OD and 20/40 OS. Mild corneal clouding was noted. Fundus photography and spectral-domain optical coherence tomography showed choroidal deposits in both eyes (Figure). Comprehensive visual electrophysiology testing had normal results. There was no progression over the next 3 years.