A 15-year-old girl was found to have temporal hemianopia of the left eye. Her visual acuity was 20/20 OU and she had normal color discrimination bilaterally. Left afferent pupillary defect was present. Right-eye perimetry results were normal, but complete temporal hemianopia respecting vertical meridian was found on the left (Figure 1). The nasal half of the left optic nerve disc showed agenesis (Figure 2). Magnetic resonance imaging revealed absent septum pellucidum, consistent with de Morsier syndrome.1
Smolyar A, Eggenberger ER, Kaufman DI. Monocular Temporal Hemianopia Associated With Optic Nerve Hypoplasia. Arch Ophthalmol. 2005;123(8):1155. doi:10.1001/archopht.123.8.1155
Customize your JAMA Network experience by selecting one or more topics from the list below.
Create a personal account or sign in to: