A 46-year-old asymptomatic woman with bilateral Snellen visual acuity of 20/20 was referred by her optician for corneal signs. She was kyphotic (Figure 1) with subcutaneous white deposits in her fingers (Figure 2). Slitlamp examination showed a Vogt white limbal girdle with adjacent white, flakelike subepithelial deposits of the limbal conjunctiva (Figure 3) bilaterally. There were peripheral curvilinear white corneal deposits of the anterior stroma spreading 3 mm centrally, evenly distributed in all clock hours (Figure 4) bilaterally.