The types of retinal degeneration in the macular region are based on differences in the ophthalmoscopic picture and also on the presence or absence of associated mental involvement. The following six cases are reported as examples of the macular type of maculocerebral degeneration (Oatman) or of progressive family degeneration in the macular region without psychic disturbance (Stargardt).
REPORT OF CASES
Case 1.—W. F., a boy, aged 11, seen on March 24, 1915, said that his sight had been failing for one year. There was no consanguinity, familial history or hemeralopia. His previous illnesses were meningitis (?), measles, mumps and cyclical albuminuria. He was a healthy-appearing, intelligent boy. Vision with correcting glasses was 20/70. The field showed a central scotoma. The optic nerve and vessels were normal. In both macular regions, there were superficial choroidal changes consisting of depigmentation and irregular pigment hypertrophy. Surrounding this area, there were many small blurred
KNAPP A. RETINAL DEGENERATION IN MACULAR REGION WITHOUT CEREBRAL SYMPTOMS. Arch Ophthalmol. 1929;1(3):311–314. doi:10.1001/archopht.1929.00810010323002
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