Since Lindau1 correlated the syndrome of hemangiomas of the cerebellum and retina (1926-1927), and Cushing and Bailey2 so recently reviewed the literature in reporting their case (1928), to include a review here seems unnecessary.
That the association of angioma of the retina with angiomatous and cystic lesions in other parts of the body, particularly with a cerebellar cyst, and its familial tendency are not generally recognized by ophthalmologists is evident from the statement of Cushing and Bailey2 that "out of many examinations during the patient's life by at least eight observers, the presence of the angioma was not detected."
The large tortuous retinal vein had been observed, but its significance was evidently not appreciated.
Cushing and Bailey,2 in reporting their case, stated that, so far as they were aware, it was the first in which the histologic diagnosis of the cerebellar lesion had been verified
ATKINSON WS. ANGIOMATOSIS RETINAE WITH CEREBELLAR CYST (LINDAU'S DISEASE). Arch Ophthalmol. 1932;7(4):510–514. doi:10.1001/archopht.1932.00820110022002
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