Naevus flammeus associated with glaucoma has been recognized since 1860, when Schirmer1 reported a case of nevus of the face and buphthalmus. Since then about sixty-five cases have been reported, and in these fifteen eyeballs have been examined histologically.
By naevus flammeus, or port wine nevus, is meant a congenital anomaly manifesting itself as a purple discoloration of more or less extensive areas of the skin, the anatomic basis of which consists of telangiectatic vessels. This malformation is more common on the face than on the body and is most often confined to one side of the face, with the median line as its boundary. Not infrequently a striking agreement may be observed between the nevus and the distribution of one or more branches of the trigeminal nerve.
The glaucoma which is associated with this condition is chronic and noninflammatory or primary. The age at which the ocular hypertension
MEHNEY GH. NAEVUS FLAMMEUS ASSOCIATED WITH GLAUCOMA: REPORT OF A CASE. Arch Ophthalmol. 1937;17(6):1018–1023. doi:10.1001/archopht.1937.00850060074006
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