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Article
June 1940

GYRATE ATROPHY OF THE RETINA AND CHOROID FOLLOWING RETINITIS PIGMENTOSA: REPORT OF TWO CASES

Author Affiliations

WASHINGTON, D. C.
From the Department of Ophthalmology of the George Washington University School of Medicine.

Arch Ophthalmol. 1940;23(6):1252-1256. doi:10.1001/archopht.1940.00860131410014
Abstract

Gyrate atrophy of the retina and choroid was first described by Cutler1 and Fuchs.2 Nettleship3 has exhaustively studied retinitis pigmentosa and allied conditions with particular reference to consanguinity and heredity. Because the symptomatology is similar, he included in his extensive study retinitis pigmentosa sine pigmento, retinitis punctata albescens (Mooren and Gayet), gyrate atrophy of the retina and the choroid (Fuchs), congenital stationary night blindness without changes and choroideremia. Other associated deficiencies which he found were deafness; deaf-mutism; various grades of mental deficiency, including idiocy and insanity ; epilepsy, and progressive paralysis, apparently spinal but not thoroughly analyzed. Also observed were polydactylism, coloboma of the iris, remnants of the hyaloid artery, congenital cataract and posterior cortical cataract without other changes, conical cornea, a peculiar condition of the skin, heterochromia of the iris and color blindness.

Bedell4 recently presented a thorough review of the literature of choroideremia, in which

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