The occurrence of bilateral glaucoma with unilateral naevus flammeus appears to be unique in American literature and has been reported only once abroad. The usual syndrome of glaucoma and naevus flammeus of the skin about the involved eye is still sufficiently uncommon to warrant recording such an association.
This syndrome, to which is frequently attached the names of Schirmer, Sturge and Weber, has been well reviewed in the English language in recent years,1 and a detailed repetition at this time is unwarranted. A brief description may, however, be appropriate.
In 1860 Schirmer first reported the association of naevus flammeus of the face with buphthalmos. Nineteen years later Sturge presented a case in which there were, in addition to the dermatologic and ocular abnormalities, epileptiform seizures involving the contralateral side of the body, attributed by him to a nevoid condition of the vessels of the brain. Weber (1928), in a
EHRLICH LH. BILATERAL GLAUCOMA ASSOCIATED WITH UNILATERAL NAEVUS FLAMMEUS: REPORT OF A CASE. Arch Ophthalmol. 1941;25(6):1002–1006. doi:10.1001/archopht.1941.00870120084004
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