The occurrence of glaucoma with nevus flammeus is uncommon, although not rare, in both the foreign and the American literature. The condition was first described by Schirmer in 1860, in association with buphthalmos, and since then several others have added to the picture to warrant its acceptance as a clinical entity, manifested by nevus flammeus, glaucoma, epileptiform seizures, nevi and dilated vessels in the conjunctiva, iris and choroid.
Of the many observations made in cases of this syndrome, few have agreed concerning the mechanism of the glaucoma; indeed, etiologic theories have varied sufficiently to permit O'Brien and Porter1 to state that the cause was unknown. From the evidence in many of the reported cases and in the present case, it appeared that perhaps another mechanism, not associated with increased intraocular pressure, may be the cause of the glaucomatous atrophy of the optic nerve.
REPORT OF CASE
The patient, aged
GROSSMANN EE. GLAUCOMA ASSOCIATED WITH NEVUS FLAMMEUS: REPORT OF A CASE. Arch Ophthalmol. 1945;33(5):389–391. doi:10.1001/archopht.1945.00890170065007
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