Heredodegenerations and Heredoconstitutional Defects of the Retina

CONTENTS 

• Heredodegenerations Involving the Elastic Layer of Bruch's Membrane

  • Kuhnt-Junius Disciform Macular Degeneration

  • Angioid Streaks

  • Cases of Sorsby and Mason

• Heredodegenerations of the Neuroepithelium

  • Heredodegeneration of the Macula Lutea

  • Primary Pigmentary Degeneration of the Retina Laurence-Moon-Biedl Syndrome

  • Gyrate Atrophy of the Choroid and the Retina

  • Choroideremia

• Heredoconstitutional Defects of the Neuroepithelium

  • Congenital Night Blindness Without Fundus Changes

  • Oguchi's Disease: Congenital Night Blindness with Grayish-White Discoloration of the Fundus

  • Retinitis Punctata Albescens

• Heredodegeneration of the Inner Nuclear Layer

  • Cystoid Degeneration of the Retina

  • Retinitis Circinata

• Heredodegeneration of the Ganglion Cells of the Retina

  • Infantile Amaurotic Family Idiocy, or Tay-Sachs Disease

  • Juvenile Amaurotic Family Idiocy (Vogt-Spielmeyer or Stock-Spielmeyer Type)

  • Late Infantile Amaurotic Family Idiocy (Bielschowsky, or Batten-Mayou Type)

  • Niemann-Pick Disease

INTRODUCTION  Degenerations of the retina on a hereditary basis present a variety of problems (1) as to the character of the hereditary factors, (2) as to the ultimate factors in the pathogenesis,