[Skip to Navigation]
November 1959

Nystagmus Retractorius

Author Affiliations

Present address, Dr. Smith: Wilmer Institute of Ophthalmology, The Johns Hopkins Hospital, Baltimore (5).; From the Howe Laboratory of Ophthalmology, Harvard University Medical School; Neurology Service, Lemuel Shattuck Hospital, and Neurology Service, Massachusetts General Hospital.

AMA Arch Ophthalmol. 1959;62(5):864-867. doi:10.1001/archopht.1959.04220050124020

The Koerber-Salus-Elschnig Sylvian aqueduct syndrome1 consists of the following findings:

1. Paresis of vertical gaze

2. Pupillary abnormalities

3. Tonic spasm of convergence on attempted upward gaze

4. Clonic convergence movements, or convergence nystagmus

5. Nystagmus retractorius

6. Vertical nystagmus on gaze up or down

7. Extraocular muscle pareses

This is a report of two recently encountered cases of this rare entity in which nystagmus retractorius was associated with retraction of the upper lids. A unique optokinetic response, which to our knowledge has not been reported, was present in both patients.

Report of Cases 

Case 1.  —This 60-year-old white woman was seen through the courtesy of the neurology service at the Lemuel Shattuck Hospital. Except for asymptomatic hypertension for many years, she was in good health until Feb. 10, 1959, when she suddenly developed a headache at work and her eyes were noted to turn in. She rapidly became

Add or change institution