The location of the tumor of von Hippel's disease in the optic papilla or juxtapapillary retina is very uncommon.1 A survey of the literature reveals only 14 recorded cases,2-13 of which ten are documented by histopathologic study (Table). The lesions were unilateral in all the cases. There seems to be a predilection for the temporal portion of the disc by these tumors, in that eight of the 14 involved the temporal half of the disc and juxtapapillary retina. Of the remaining five cases, two were stalked, two involved the inferior disc margin and adjacent retina, and two resided in the nasal portion of the papilla. This paper reports the first example of bilateral optic disc involvement in von Hippel's disease.
Report of Case
A 29-year-old white Army enlisted man first noted the onset of blurred vision in his right eye in early 1959. Ophthalmoscopic examination revealed bilateral papilledema
DARR JL, HUGHES RP, McNAIR JN. Bilateral Peripapillary Retinal HemangiomasA Case Report. Arch Ophthalmol. 1966;75(1):77–81. doi:10.1001/archopht.1966.00970050079015