Operative treatment of congenital jerk-type nystagmus with ocular torticollis is discussed. The mechanism causing the head turn, methods used in measurement of the head and eye deviation, as well as the selection of the surgical procedures indicated are analyzed. A review of the ophthalmic literature on the subject is included with particular emphasis on the original work and theories of Kestenbaum, Anderson, and Goto. The results of seven cases operated on for this condition utilizing our techniques are presented.