ENCEPHALOCELES are lesions that usually cause signs and symptoms that are misleading.1 The cranial contents may herniate through one of the natural openings, such as the optic foramen or the sphenoid fissure, or through an embryonic defect in the bony orbit.2 Anteriorly, a transethmoidal defect may occur through the lamina cribrosa and present as an orbital tumor. This report describes a case of an ethmoid encephalocele presenting as an orbital tumor.
Report of a Case
This 62-year-old white woman was in good health until three weeks prior to admission, when a tender swelling developed rather suddenly in the superior nasal aspect of her right orbit (Fig 1). On the previous day, she had been mowing her lawn and had gotten grass in her nose causing her to sneeze and have hayfever like symptoms. Because of her past history of sinus trouble, she was considered to have acute ethmoiditis
Leone CR, Marlowe JF. Orbital Presentation of an Ethmoidal Encephalocele: Report of a Case of a 62-Year-Old Woman. Arch Ophthalmol. 1970;83(4):445–447. doi:10.1001/archopht.1970.00990030445009
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