• Reticular dystrophy of the retinal pigment epithelium is characterized by a posterior pattern of pigment clumping like a "fishnet with knots." Four patients in three successive generations were seen with typical reticular dystrophy. A fifth patient had abnormal dark adaptation. In this family reticular dystrophy was characterized by the typical reticular pigmentary pattern, good visual acuity, normal electroretinographic findings, abnormal electro-oculographic findings, and abnormal dark adaptation. The pedigree indicates autosomal dominance as the inheritance pattern.
Kingham JD, Fenzl RE, Willerson D, Aaberg TM. Reticular Dystrophy of the Retinal Pigment EpitheliumA Clinical and Electrophysiologic Study of Three Generations. Arch Ophthalmol. 1978;96(7):1177–1184. doi:10.1001/archopht.1978.03910060011003
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