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March 1983

Hereditary Posterior Microphthalmos With Papillomacular Fold and High Hyperopia

Author Affiliations

From the Department of Ophthalmology, Jules Stein Eye Institute, UCLA Center for the Health Sciences (Drs Spitznas and Bateman); and the University Eye Hospital, Essen, Germany (Dr Gerke).

Arch Ophthalmol. 1983;101(3):413-417. doi:10.1001/archopht.1983.01040010413014

• Five patients had a bilateral hereditary ocular syndrome composed of posterior microphthalmos with a papillomacular fold and high hyperopia. Anterior segment dimensions were near normal; the vitreous compartment was markedly foreshortened. A papillomacular retinal fold extending from the center of the fovea toward the optic nerve head was present. Visual acuity ranged from 0.05 (20/400) to 0.6 (20/33); refractive errors ranged from +11.25 to +17.50 diopters. An autosomal recessive pattern of inheritance is postulated.

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